English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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Pemphigus Vegetans in the Inguinal Folds.
CiteScore measures average citations received per document published. Prognosis Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions. Over several days, the center of the lesions sinks and develops a characteristic morphology: Disease definition Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.
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Orphanet: Enfermedad de Degos
Face, scalp, palms of hands and soles of feet are rarely involved. More developed lesions can imitate lichen sclerosus see this term. Genetic counseling A genetic predisposition with an autosomal dominant trait has been suggested. Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs.
Term Bank – enfermedad de degos – Spanish English Dictionary
The etiopathogenesis of the disease remains unknown. Show more Show less. Summary and related texts.
The histology of early lesions resembles cutaneous lupus erythematosus see this term. This item has received. SRJ is a prestige metric based on the idea that not all citations are the same.
Subscriber If you already have your login data, please click here. Check this box if you wish to receive a copy of your message. Health care resources for this disease Expert centres 69 Diagnostic tests 0 Patient organisations 21 Orphan drug s 0. Go to the members area of the website of the Dego, https: Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted. Are you a health professional able to prescribe dd dispense drugs? SJR uses a similar algorithm as the Google page rank; it provides a quantitative and qualitative measure of the journal’s impact.
Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. Management and treatment Therapeutic efforts with anticoagulants and compounds enfermevad facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
Print Send to a friend Export reference Mendeley Statistics. For all other comments, please send your remarks via contact us. Ocular involvement, which affects the eyelids, conjuctiva, retina, sclera and the choroid plexus, as well as the development of diplopia and ophthalmoplegia as secondary side effects of the neurologic involvementhas also been described.
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No effective treatment for the systemic manifestations has been established, however, subcutaneous treprostinil has been tested successfully in one case with intestinal and CNS manifestations.
May Pages ee22 Pages Additional information Further information on this disease Classification s 3 Gene s 0 Clinical signs and symptoms Publications in PubMed Other website s 7.
Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Subscribe to our Newsletter. More developed lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis and an area of sclerosis in the papillary dermis.
enfermedad de degos
Systemic manifestations are progressive and may lead to serious complications: Idiopathic, monosymptomatic, cutaneous presentations enfermeadd benign, however, systemic manifestations can develop years after the occurrence of skin lesions.
From Monday to Friday from 9 a. Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed. You can change the settings or obtain more information by clicking here. In the year has been indexed in the Medlinedatabase, and has become a vehicle enfermedd expressing the most current Spanish medicine and modern. Etiology The etiopathogenesis of the disease remains unknown. Differential diagnosis The histology of early lesions enfermdead cutaneous lupus erythematosus see this term.
Clinical description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities. Continuing navigation will be considered as acceptance of this use. SNIP measures contextual citation impact by wighting citations based on the total number of citations in a subject field.
Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, enfermedsd, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases. Specialised Social Services Eurordis directory. Diagnostic methods Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. Summary Epidemiology Less than cases have been described in the literature.